Dandy-Walker Malformation With Postaxial Polydactyly: Newborn Case Report

نویسندگان

چکیده

Dandy-Walker malformation is a rare congenital malformation, characterized by agenesis or hypoplasia of the cerebellar vermis, cystic dilatation 4th ventricle and enlargement posterior fossa. Postnatal hydrocephalus develops in approximately 70-90% patients. The relationship with postaxial polydactyl has been defined as possible autosomal recessive syndrome (OMIM 220220). Here, we present an infant accompanying because rare.

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ژورنال

عنوان ژورنال: A?BÜ ?zzet Baysal t?p fakültesi dergisi

سال: 2021

ISSN: ['1305-4392']

DOI: https://doi.org/10.47493/abantmedj.950391